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【文章內(nèi)容簡介】 Factor XIIa Factor XII Factor XIIa Prekallikrein Kallikrein HK Bradykinin Factor XIIf C1 C1 C4, C2 digestion Surface Surface Inhibited By C1 INH Plasmin Plasminogen Further Data Regarding C1 INH ? Complete acid sequence known。 heavily glycosylated ? Generation of cDNA clones acplished, localization to chromosome 11 ? Deficiency heterogeneous by DNA restriction fragment length polymorphisms ? Deficiency frequently associated with autoimmune phenomena ? Mechanisms of acquired C1 inhibitor deficiency: ? Depletion by plement activation ? Contact system activation ? AntiC1 inhibitor antibodies ? Antiidi
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