【新整理】多囊性腎臟病變ppt課件-展示頁(yè)
2024-11-19 00:18本頁(yè)面
【正文】 l or bilateral renal cysts (bilateral involvement is more common in the genetically inherited conditions) ● size of the kidneys—are they large or small? ● localization to one part of the kidney or diffuse involvement of the whole kidney. Is there a capsule around the cysts? ● extrarenal cysts, in particular in the liver or pancreas ● liver size and hepatic parenchyma appearance ● presence of a large spleen and portal hypertension.,Renal cysts are common and may be hereditary,developmental or acquired. The classification of cystic renal disease varies according to the perspective from which it is written, and despite a vast amount of literature on the subject, there is still no generally accepted classification in existence. The early Potter classification is of limited value for clinical practice because not all types represent clinical entities.,The following classification is by no means all inclusive but aims to emphasize the important clinical cystic disorders likely to be encountered by the sonographer. Broadly speaking, cystic disease of the kidneys can be divided into two groups genetic disease and nongenetic disease:,● Genetic disease —autosomal recessive polycystic kidney disease (ARPKD) —autosomal dominant polycystic kidney disease (ADPKD) —juvenile nephronophthisis and medullary cystic disease complex —glomerulocystic kidney disease —cysts with multiple malformation syndromes。,● Nongenetic disease —simple cysts —multicystic dysplastic kidney —multilocular cysts —acquired renal cystic disease (chronic renal failure) —caliceal diverticulum —medullary sponge kidney.,Genetic disease,Autosomal recessive polycystic kidney disease (ARPKD) This is a generalized cystic dilation of the renal collecting tubules so that the kidneys are packed to a greater or lesser degree with tiny little cysts (Fig. 3.31). It is much rarer than the autosomal dominant form and occurs in 1 in 50 000 people. Prenatal diagnosis can be made but there are false positive and false negative diagnoses. Congenital hepatic fibrosis is a prerequisite for the d
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