郭yl范可尼綜合征韋尼克綜合征-展示頁(yè)
2024-08-30 14:31本頁(yè)面
【正文】 引起的 腦病 。 ?II型臨床表現(xiàn)：除陰離子間隙正常的高氯性代謝性酸中毒外， 骨病 發(fā)生率在 20%左右，主要為骨軟化癥或骨質(zhì)疏松。如多發(fā)性骨髓瘤、 Wilson病、甲狀旁腺功能亢進(jìn)等。 ?糾正低血容量范可尼綜合征常因多尿而致脫水，除了針對(duì)病因治療外，應(yīng)補(bǔ)足含鹽的液體（包括鈉、鉀、鈣等），可采用定時(shí)口服，必要時(shí)臨時(shí)追加。 ?糾正酸中毒根據(jù)碳酸氫根丟失情況補(bǔ)充堿劑，可用碳酸氫鹽、枸櫞酸鹽、乳酸鹽等，分次給服，以血中碳酸氫鹽水平恢復(fù)正常為標(biāo)準(zhǔn)。青霉胺可試用于消除胱氨酸，但不能減少細(xì)胞內(nèi)胱氨酸沉著；二硫蘇糖醇（ DDT）療效欠佳，半胱氨酸效果較好。s disease and Lowe syndrome, are X linked. ?A recently described form of this disease is due to a mutation in EHHADH，decreasing the production of ATP. 范可尼綜合征 Acquired ?It is possible to acquire this disease later in life. ?Causes include ingesting expired tetracyclines which damage proximal tubule, and as a side effect of tenofovir. ?Lead poisoning also leads to Fanconi syndrome. ?Multiple myeloma or monoclonal gammopathy of undetermined significance can also cause the condition. ?Additionally, Fanconi Syndrome can develop as a secondary or tertiary effect of certain autoimmune disorders. 范可尼綜合征 ?Wilson病或重
環(huán)評(píng)公示相關(guān)推薦
鄂ICP備17016276號(hào)-1