家裝電工基礎知識ppt課件-資料下載頁
2025-05-02 18:04本頁面
【正文】 eufeld, who was then at the National Institutes of Health, showed that the lysosomal enzymes of persons with Icell disease emerge from the Golgi apparatus without the chemical tag they need to be directed to the lysosomes. She also showed that the defect could be corrected in testtube cultures of cells taken from people with the disease. The corrective factors she supplied were the specific, properly tagged enzymes that the cells lacked. ? Although enzyme replacement therapy is not being used to treat people with lysosomal storage diseases like Hurler39。s syndrome, it is being used to treat a different group of disorders called lipid storage diseases. Enzyme replacement therapy for many disorders presents challenges to researchers, however, because purified enzymes injected directly into the body tend to be quickly destroyed or inactivated. ? It is particularly difficult to get enzymes into brain cellsan important problem now under investigation, since several lysosomal storage diseases produce severe mental retardation. ? 四 過氧化物酶體 ? 微體或過氧化氫體 ? （ peroxisome） ? 一、微體由單層膜包圍，中有一些中等致密度的顆 ? 粒狀物質和結晶狀結構的囊狀小體，所含物質主要 ? 有過氧化氫酶和其它一些氧化酶。 ? 二、功能：解毒作用 ? ? 微體 在植物細胞稱園球體 乙醛酸循環(huán)體為微體 ? 1. 過氧化物酶體和溶酶體的區(qū)別 P189 ? ? (1) 解除過氧化氫的毒害 氧化酶 過氧化氫酶 O178。 ? O178。 H178。O178。 2H178。O ? RH 178。 R H178。O178。 ? (2) 分解脂肪酸為細胞提供熱量 ? (3) 在植物細胞中的作用 The structure and function of peroxisomes. 3 peroxisomes的發(fā)生 190
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